| Indications |
Product |
Recommended
Age Group |
|
Description |
| ■
Glutaric Acidemia Type I |
XLys,
XTrp AnalogTM |
Infants |
|
lysine-
and tryptophan-free powdered infant formula |
XLys,
XTrp Maxamaid®
(orange) |
Toddlers
and young children |
|
lysine-
and tryptophan-free powdered medical food |
XLys,
XTrp, Maxamum®
(orange) |
Older
children and adults |
|
lysine-
and tryptophan-free powdered medical food |
| ■
Hypermethionemia & Homocystinuria |
XMet
Analog |
Infants |
|
methionine-free
powdered infant formula |
XMet
Maxamaid
(orange) |
Toddlers
and young children |
|
methionine-free
powdered medical food |
XMet
Maxamum
(orange) |
Older
children and adults |
|
methionine-free
powdered medical food |
| ■
Isovaleric Acidemia |
XLeu
Analog |
Infants |
|
leucine-free
powdered infant formula |
| |
XLeu
Maxamaid
(orange) |
Toddlers
and young children |
|
leucine-free
powdered medical food |
| |
XLeu
Maxamum
(orange) |
Older
children and adults |
|
leucine-free
powdered medical food |
■ Long
Chain Fatty Acid
Oxidation Disorders |
Monogen |
Individuals
over 1 year |
|
Low
fat, high MCT powdered medical food |
| ■ Maple Syrup Urine Disease (MSUD) |
MSUD
Analog |
Infants |
|
valine-,
leucine-, and isoleucine-free powdered infant formula |
Acerflex®
(pineapple) |
Toddlers
and children |
|
valine-,
leucine-, and isoleucine-free powdered medical food |
MSUD
Maxamaid
(orange) |
Toddlers
and young children |
|
valine-,
leucine-, and isoleucine-free powdered medical food |
MSUD
Maxamum
(orange) |
Older
children and adults |
|
valine-,
leucine-, and isoleucine-free powdered medical food |
| ■ Phenylketonuria
(PKU) |
XPhe
Analog |
Infants |
|
phenylalanine-free
powdered infant formula |
Periflex® Junior
(Unflavored, orange and chocolate) |
Toddlers
and young children |
|
phenylalanine-free
powdered medical food |
Periflex
Advance
(Unflavored, orange and chocolate) |
Older
children and adults |
|
phenylalanine-free
powdered medical food |
XPhe
Maxamaid
(unflavored, orange and strawberry) |
Toddlers
and young children |
|
phenylalanine-free
powdered medical food |
XPhe
Maxamum
(unflavored and orange) |
Older
children and adults |
|
phenylalanine-free
powdered medical food |
XPhe
Maxamum Drink
(berry and orange) |
Children
over 5 years and adults |
|
phenylalanine-free
ready-to-drink medical food |
Lophlex®
(berry and orange) |
Older
children and adults |
|
phenylalanine-free
powdered medical food |
| Phlexy-10® Add-InsTM |
Children over 3 years and adults |
|
|
phenylalanine-free,
flavorless powdered medical food |
Phlexy
- 10 Drink Mix
(blackcurrant/Apple and
Tropical Surprise) |
Children
and adults |
|
phenylalanine-free
powdered medical food |
| Phlexy
- 10 Capsules |
Children
and adults |
|
phenylalanine-free
amino acid-based medical food in capsule form |
LanaflexTM
(orange) |
Adults |
|
phenylalanine-free
powdered medical food, containing the remaining large neutral
amino acids |
| ■
Propionic & Methylmalonic Acidemia |
XMTVI
Analog |
Infants |
|
methionine-,
threonine-, and valine-free, isoleucine-low powdered infant
formula |
XMTVI
Maxamaid
(orange) |
Toddlers
and young children |
|
methionine-,
threonine-, and valine-free, isoleucine-low powdered medical
food |
XMTVI
Maxamum
(orange) |
Older
children and adults |
|
methionine-,
threonine-, and valine-free and isoleucine-low powdered medical
food |
| ■ Tyrosinemia |
|
|
|
|
| |
Type
I |
XPTM
Analog |
Infants |
|
phenylalanine-,
tyrosine-, and methionine-free powdered infant formula |
| |
Type
I & II |
XPhe,
XTyr Analog |
Infants |
|
phenylalanine- and tyrosine-free powdered
infant formula |
|
| |
|
XPhe,
XTyr Maxamaid
(orange) |
Toddlers
and young children |
|
phenylalanine-
and tyrosine-free powdered medical food |
| |
Type
II |
XPhen,
XTyr Maxamaid |
Toddlers
and young children |
|
phenylalanine-
and tyrosine-free powdered medical food enriched w/ vitamins
and minerals |
| |
|
XPhen,
XTyr Maxamum |
Children
and adults |
|
phenylalanine-
and tyrosine-free powdered medical food enriched w/ vitamins
and minerals |
| ■ Modular
Diets |
Complete
Amino Acid Mix |
Children
and adults |
|
unflavored,
powdered medical food containing essential and non-essential
amino acids |
| Essential
Amino Acid Mix |
Children
and adults |
|
unflavored,
powdered medical food containing essential amino acids, including
cystine and histidine |
| Duocal |
Children
and adults |
|
powdered
energy source containing fat and carbohydrate |
| Polycal |
Children
and adults |
|
powdered
carbohydrate energy source |
| Protifar |
Children
and adults |
|
powdered,
concentrated protein source based on milk protein |
