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MSUD Maxamum

MSUD Maxamum

A Valine-, Leucine-, and Isoleucine-Free powdered medical food for the dietary management of maple syrup urine disease (MSUD) in children over 8 years and adults, including maternal patients.

Main Features
  • Isoleucine-, leucine- and valine-free
  • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.
  • MSUD Maxamum provides 40 g of protein equivalent per 100 g of powder
  • Pleasant orange flavoured powder
  • Does not contain fat thereby allowing greater flexibility in modifying energy intake.
  • Osmolality (mOsm/kg) :
    •   Dilution  
      1 to 7 800 mOsm/kg
      1 to 5 1130 mOsm/kg

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Indication(s)
  • Maple Syrup Urine Disease

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Directions for Preparation and Use

Maxamum must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrient requirements.

The recommended intake of Maxamum will vary depending on the age, bodyweight and medical condition of the individual. Intake should be adjusted to maintain normal growth and development. For accuracy, Maxamum should be weighed on a gram scale. The daily intake of Maxamum should be divided into equal portions and distributed throughout the day.

Maxamum is best served with meals. Make a paste of the prescribed amount of powder with a small volume of chilled water. Gradually add sufficient water to make the desired volume. It is recommended that Maxamum be prepared at a 1 to 7 dilution (e.g. 35 g (approx ¼ cup) of powder plus 245 mL (approx. 8 fl oz) of water) and advanced to a 1 to 5 dilution (e.g. 35 g (approx ¼ cup) of powder plus 175 mL (approx. 6 fl oz) of water). These dilutions are guidelines only. Maxamum may be given in a more concentrated form (e.g. drink or paste). If so, water or diluted drinks should be offered at the same time. For best taste, consume immediately. Larger volumes of prepared drink mix should be refrigerated and used within 24 hours or preparation.

Maxamum Range
(Flavoured & Unflavoured)
Measure Weight
1 Cup 145 g
1/2 Cup 70 g
1/4 Cup 35 g
1 Tbsp 9 g

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Precaution
  • Must only be consumed by individuals with proven maple syrup urine disease while under strict medical supervision. Not intended for children under nine years of age. Not suitable as a sole source of nutrition. Not for parenteral use.

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Storage
  • Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

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Nutrients
Nutrients Per 100 g
Calories 305
Protein Equivalent, g 40
Fat, g <1
Carbohydrate, g 34

Amino Acid Profile, g  
L-Alanine 2.4
L-Arginine 4.1
L-Aspartic Acid 3.4
L-Cystine 1.6
L-Glutamic Acid 4.6
Glycine 3.7
L-Histidine 2.3
L-Isoleucine None
L-Leucine None
L-Lysine 4.2
L-Methionine 0.99
L-Phenylalanine 2.8
L-Proline 4.5
L-Serine 2.8
L-Threonine 3.1
L-Tryptophan 1.3
L-Tyrosine 2.8
L-Valine None
L-Glutamine 0.32
L-Carnitine, mg 39
Taurine, mg 140

Vitamins Per 100 g
Vitamin A, IU 2228
Vitamin D3, IU 332
Vitamin E, IU 18.3
Vitamin K, mcg 82
Thiamine, mg 0.91
Riboflavin, mg 0.97
Vitamin B6, mg 1.6
Vitamin B12, mcg 3.1
Niacin, mg 5.7
Folic Acid, mcg 491
Pantothenic Acid, mg 4.9
Biotin, mcg 24.5
Vitamin C, mg 62
Choline, mg 430
Inositol, mg 80

Minerals Per 100 g
Calcium, mg
1183
Phosphorus, mg
1137
Magnesium, mg
306
Iron, mg
14.7
Zinc, mg
9
Manganese, mg
1.8
Copper, mcg
820
Iodine, mcg
131
Molybdenum, mcg
37
Chromium, mcg
26
Selenium, mcg
58
Sodium, mg
560
Potassium, mg
700
Chloride, mg
560

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Ingredients

Sugar, L-Lysine L-Glutamate, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Proline, L-Arginine, Glycine, L-Aspartic Acid, L-Threonine, L-Phenylalanine, L-Tyrosine, L-Serine, Artificial Flavour, L-Histidine, L-Alanine, Citric Acid, Magnesium Acetate, L-Cystine, L-Tryptophan, Tripotassium Citrate, Choline Bitartrate, L-Methionine, Sodium Chloride, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, L-Glutamic Acid, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium D-Pantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamine Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.

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Ordering Information
  • For product information or to place an order please call 1-877-636-2283 or fax 514-745-6625 Monday to Friday, 8:30 to 5:00 EST

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