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XMTVI
Maxamaid

A
methionine-, threonine-, valine-free and isoleucine-low powdered
medical food for the dietary management of vitamin B12
non-responsive methylmalonic acidemia or propionic acidemia in children
aged 1 to 8 years.
- Methionine-,
threonine-, valine-free and isoleucine-low
- Contains
a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements
- XMTVI
Maxamaid provides 25 g of protein equivalent per 100 g of
powder
- Pleasant
orange flavoured powder
- Does
not contain fat thereby allowing greater flexibility in modifying
energy intake
- Osmolality:
| |
Dilution |
|
| |
1
to 7 |
680
mOsm/kg |
| |
1
to 5 |
940
mOsm/kg |
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- Vitamin
B12 non-responsive methylmalonic acidemia
- Propionic
acidemia
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Directions
for Preparation and Use
Maxamaid
Range
(Flavoured & Unflavoured)
| Measure |
Weight |
| 1
Cup |
145
g |
| 1/2
Cup |
70
g |
| 1/4
Cup |
35
g |
| 1
Tbsp |
9
g |
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| Nutrients |
Per
100 g |
| Calories |
350 |
| Amino
Acids, g |
28.6 |
| Protein
Equivalent, g |
25 |
| Fat,
g |
<0.5 |
| Carbohydrate,
g |
62 |
| Amino
Acid Profile, g |
Per
100 g |
| L-Alanine |
2.89 |
| L-Arginine |
2.59 |
| L-Aspartic
Acid |
2.3 |
| L-Cystine |
0.95 |
| L-Glutamic
Acid |
2.86 |
| Glycine |
1.16 |
| L-Histidine |
1.75 |
| L-Isoleucine |
<0.07 |
| L-Leucine |
3.9 |
| L-Lysine |
2.65 |
| L-Methionine |
None |
| L-Phenylalanine |
1.72 |
| L-Proline |
1.16 |
| L-Serine |
1.62 |
| L-Threonine |
None |
| L-Tryptophan |
0.76 |
| L-Tyrosine |
1.72 |
| L-Valine |
None |
| L-Carnitine |
0.02 |
| Taurine |
0.14 |
| L-Glutamine |
0.28 |
|
Vitamins |
Per
100 g |
| Vitamin
A, IU (mcg R.E.) |
1665
(500) |
| Vitamin
D3, IU (mcg) |
480
(12) |
| Vitamin
E, IU (mg α-T.E.) |
6.5
(4.4) |
| Vitamin
K, mcg |
35 |
| Thiamine,
mg |
1.1 |
| Riboflavin,
mg |
1.2 |
| Vitamin
B6, mg |
1 |
| Vitamin
B12, mcg |
2 |
| Niacin,
mg |
12 |
| Folic
Acid, mcg |
150 |
| Pantothenic
Acid, mg |
3.7 |
| Biotin,
mcg |
120 |
| Vitamin
C, mg |
135 |
| Choline,
mg |
110 |
| Inositol,
mg |
56 |
| Minerals |
Per
100 g |
| Calcium,
mg |
810 |
| Phosphorus,
mg |
810 |
| Magnesium,
mg |
200 |
| Iron,
mg |
12 |
| Zinc,
mg |
13 |
| Manganese,
mg |
1.3 |
| Copper,
mcg |
2000 |
| Iodine,
mcg |
90 |
| Molybdenum,
mcg |
45 |
| Chromium,
mcg |
45 |
| Selenium,
mcg |
40 |
| Sodium,
mg (mEq) |
580
(25) |
| Potassium,
mg (mEq) |
840
(22) |
| Chloride,
mg (mEq) |
450
(13) |
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Sugar,
Corn Syrup Solids, L-Lysine-L-Glutamate, Citric Acid, L-Leucine,
Calcium Phosphate Dibasic, L-Alanine, Trisodium Citrate, L-Arginine,
L-Aspartic Acid, L-Histidine, L-Phenylalanine, L-Tyrosine, L-Serine,
Magnesium Hydrogen Phosphate, Glycine, L-Proline, Artificial Flavour,
Tripotassium Citrate, Potassium Chloride, L-Cystine, L-Tryptophan,
Tricalcium Citrate, Choline Bitartrate, L-Glutamine, L-Glutamic
Acid, L-Ascorbic Acid, Taurine, Tricalcium Phosphate, Ferrous
Sulfate, M-Inositol, Zinc Sulfate, L-Carnitine, Niacinamide, DL-Alpha
Tocopheryl Acetate, Cupric Sulfate, Manganese Sulfate, Calcium
D-Pantothenate, Pyridoxine Hydrochloride, Thiamine Chloride Hydrochloride,
Riboflavin, Vitamin A Acetate, Artificial Colors (Beta Carotene,
Beet Red), Chromium Sulfate, Folic Acid, Potassium Iodide, D-Biotin,
Sodium Molybdate, Sodium Hydrogen Selenite, Phylloquinone, Vitamin
D3, Cyanocobalamin.
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