Products

Condition

Recommended Age Group

Product Description

• Phenylketonuria (PKU)

Infants birth to one year

A phenylalanine-free powdered infant formula

• Phenylketonuria (PKU)

Infants birth to one year

A phenylalanine-free powdered infant formula with iron

Periflex® Junior (unflavored, orange and chocolate)

• Phenylketonuria (PKU)

Toddlers and young children

A phenylalanine-free powdered medical food

Periflex® Advance (unflavored, orange and chocolate)

• Phenylketonuria (PKU)

Older children and adults, including pregnant women and women of child-bearing age

A phenylalanine-free powdered medical food

XPhe Maxamaid® (unflavored, orange and strawberry)

• Phenylketonuria (PKU)

Toddlers and young children

A phenylalanine-free powdered medical food

XPhe Maxamum® (unflavored and orange)

• Phenylketonuria (PKU)

Older children and adults, including pregnant women and women of child-bearing age

A phenylalanine-free powdered medical food

XPhe Maxamum Drink® (orange and berry)

• Phenylketonuria (PKU)

Children and adults, including pregnant women and women of child-bearing age

A phenylalanine-free ready-to-drink medical food

Lophlex™
(berry and orange)

• Phenylketonuria (PKU)

Older children and adults, including pregnant women and women of child-bearing age

A low volume phenylalanine-free powdered medical food

PKU Lophlex™ LQ

• Phenylketonuria (PKU)

Individuals over 4 years of age

A phenylalanine-free ready-to-drink medical food

Phlexy-10® Drink Mix (blackcurrent/apple and tropical sunrise)

• Phenylketonuria (PKU)

Individuals over 1 year of age, including pregnant women and women of child-bearing age

A phenylalanine-free powdered medical food

• Phenylketonuria (PKU)

Individuals over 1 year of age, including pregnant women and women of child-bearing age

A phenylalanine-free amino acid-based medical food in bar form

• Phenylketonuria (PKU)

Individuals over 1 year of age, including pregnant women and women of child-bearing age

A phenylalanine-free amino acid-based medical food in capsule form

• Phenylketonuria (PKU)

Individuals over 1 year of age, including pregnant women and women of child-bearing age

A phenylalanine-free amino acid-based medical food in tablet form

• Phenylketonuria (PKU)

Individuals over 4 years of age, including pregnant women and women of child-bearing age

A phenylalanine-free, flavorless powdered medical food containing vitamins and minerals

• Phenylketonuria (PKU)

Individuals over 11 years of age

A concentrated, powdered vitamin, mineral and trace element preparation

Lanaflex™  
(orange)

• Phenylketonuria (PKU)

Individuals over 12 years of age

A phenylalanine-free powdered medical food containing the remaining essential amino acids (large neutral amino acids and lysine)

• Phenylketonuria (PKU)

Children

An unflavored phenylalanine-free powdered medical food containing a mixture of pure L-amino acids free from phenylalanine, and enriched with vitamins, minerals and trace elements

• Phenylketonuria (PKU)

Older children and adults, including pregnant women and women of child-bearing age

An unflavored phenylalanine-free powdered medical food containing a mixture of pure L-amino acids free from phenylalanine, and enriched with vitamins, minerals and trace elements

• Maple Syrup Urine Disease (MSUD)

Infants birth to one year

A valine-, leucine-, and isoleucine-free powdered infant formula

MSUD Maxamaid® (orange)

• Maple Syrup Urine Disease (MSUD)

Toddlers and young children

A valine-, leucine-, and isoleucine-free powdered medical food

MSUD Maxamum® (orange)

• Maple Syrup Urine Disease (MSUD)

Older children and adults, including pregnant women and women of child-bearing age

A valine-, leucine-, and isoleucine-free powdered medical food

Acerflex® 
(pineapple)

• Maple Syrup Urine Disease (MSUD)

Individuals over 1 year of age

A valine-, leucine-, and isoleucine-free powdered medical food

• Maple syrup urine disease (classic, inherited and intermittent forms)
• Hypervalinemia (isoleucine and leucine should be added)
• Alpha-Methylacetoacetic aciduria (leucine and valine should
  be added)
• Ketotic hypoglycemia (leucine induced, idiopathic form)
  (isoleucine and valine should be added)
• Hyperprolinemia type II, with hyperleucine-isoleucinemia (valine should be added)

Children and adults, including pregnant women and women of child-bearing age

An unflavored valine-, leucine-, and isoleucine-free powdered medical food enriched w/ vitamins, minerals and trace elements

• Maple Syrup Urine Disease (MSUD)

Individuals over 1 year of age

An unflavored valine-, leucine-, and isoleucine-free powdered medical food

• Isovaleric Acidemia
• Other proven disorders of leucine metabolism

Infants birth to one year

A leucine-free powdered infant formula

XLeu Maxamaid ®
(orange)

• Isovaleric Acidemia
• Other proven disorders of leucine metabolism

Toddlers and young children

A leucine-free powdered medical food

XLeu Maxamum®
(orange)

• Isovaleric Acidemia
• Other proven disorders of leucine metabolism

Older children and adults, including pregnant women and women of child-bearing age

A leucine-free powdered medical food

• Glutaric Acidemia Type I

Infants birth to one year

A lysine- and tryptophan-free powdered infant formula

XLys, XTrp Maxamaid® (orange)

• Glutaric Acidemia Type I

Toddlers and young children

A lysine- and tryptophan-free powdered medical food 

XLys, XTrp Maxamum® (orange)

• Glutaric Acidemia Type I

Older children and adults, including pregnant women and women of child-bearing age

A lysine- and tryptophan-free powdered medical food

• Vitamin B6 non-responsive Homocystinuria
• Hypermethioninemia

Infants birth to one year

A methionine-free powdered infant formula

XMet Maxamaid®
(orange)

• Vitamin B6 non-responsive Homocystinuria
• Hypermethioninemia

Toddlers and young children

A methionine-free powdered medical food

XMet Maxamum®
(orange)

• Vitamin B6 non-responsive Homocystinuria
• Hypermethioninemia

Older children and adults, including pregnant women and women of child-bearing age

A methionine-free powdered medical food

• Vitamin B6 non-responsive Homocystinuria

Children and adults, including pregnant women and women of child-bearing age

An unflavored methionine-free powdered medical food enriched with vitamins, minerals, and trace elements

• Vitamin B6 non-responsive Homocystinuria
• Hypermethioninemia

Individuals over 1 year of age

An unflavored methionine-free powdered medical food

• Propionic Acidemia
• Vitamin B12 non-responsive methylmalonic acidemia

Infants birth to one year

A methionine-, threonine-, and valine-free, isoleucine-low powdered infant formula

XMTVI Maxamaid® (orange)

• Propionic Acidemia
• Vitamin B12 non-responsive methylmalonic acidemia

Toddlers and young children

A methionine-, threonine-, and valine-free, isoleucine-low powdered medical food

XMTVI Maxamum® (orange)

• Propionic Acidemia
• Vitamin B12 non-responsive methylmalonic acidemia

Older children and adults, including pregnant women and women of child-bearing age

A methionine-, threonine-, and valine-free and isoleucine-low powdered medical food

• Propionic Acidemia
• Vitamin B12 non-responsive methylmalonic acidemia

Children and adults, including pregnant women and women of child-bearing age

An isoleucine, methionine-, threonine-, and valine- free, powdered medical food enriched with vitamins, minerals, and trace elements

• Tyrosinemia, when plasma methionine level is normal

Infants birth to one year

A phenylalanine- and tyrosine-free powdered infant formula

XPhe, XTyr Maxamaid® (orange)

• Tyrosinemia, when plasma methionine level is normal

Toddlers and young children

A phenylalanine- and tyrosine-free powdered medical food

• Tyrosinemia, when plasma methionine level is above normal

Infants birth to one year

A phenylalanine-, tyrosine-, and methionine-free powdered infant formula

• Sulphite oxidase deficiency
• Other conditions requiring restriction of methionine and cystine

Infants birth to one year

A methionine- and cystine-free powdered infant formula

• Sulphite oxidase deficiency
• Other conditions requiring restriction of methionine and cystine

Individuals over one year of age

A methionine- and cystine-free powdered medical food

• Dietary management of urea cycle disorders

Children and adults, including pregnant women and women of child-bearing age

An unflavored powdered medical food containing a mixture of essential pure amino acids, enriched with vitamins, minerals, and trace elements

• Dietary management of urea cycle disorders
• Conditions in which a nutritionally complete feed is not suitable or a modular approach is required

Children and adults

An unflavored, powdered mixture of essential amino acids, including cystine and histidine

• Intractable epilepsy
• Pyruvate dehydrogenase deficiency (PDH)
• Glucose transporter type-1 deficiency

Children up to 8 years of age

A nutritionally complete, ketogenic formula in a 3:1 (fat: carbohydrate + protein) ratio; a medical food

• Intractable epilepsy
• Pyruvate dehydrogenase deficiency (PDH)
• Glucose transporter type-1 deficiency
• Other disorders where the ketogenic diet is indicated

Children and adults

A nutritionally complete, ketogenic formula in a 4:1 (fat: carbohydrate + protein) ratio; a medical food

• Intractable epilepsy
• Pyruvate dehydrogenase deficiency (PDH)
• Glucose transporter type-1 deficiency
• Other disorders where the ketogenic diet is indicated

Individuals over one year of age

A nutritionally complete, ready-to-feed ketogenic formula in a 4:1 ratio (fat:carbohydrate+ protein) contains multi-fiber system (a blend of insoluble and soluble fiber) with DHA and ARA; a medical food

• Long chain fatty acid oxidation disorders
• Hyperlipoproteinemia type 1
• Chylothorax
• Intestinal lymphangiectasia
• Intractable malabsorption with steatorrhoe
• Post-operative feeding in short gut syndrome
• Other lipid and lymphatic disorders where a low fat, high MCT diet is indicated

Individuals over one year of age

A milk protein-based powder, low in fat, and high in medium chain triglycerides (MCT); a medical food

• Failure-to-thrive
• Malabsorptive states
• Catabolic states (e.g. trauma, burns, post-op stress)
• Conditions where a high energy, low fluid, low electrolyte diet is indicated
• Protein restricted diets
• Disorders of protein and amino acid metabolism
• Modular diets
• Suitable for oral and tube feedings

Children and adults

A powdered medical food providing fat and carbohydrate for increased caloric intake.

Not nutritionally complete.

• Condition in which a nutritionally complete feed is not suitable or a modular approach is required
• Conditions where an oligoallergenic diet is indicated (e.g. individuals with intolerance to milk protein or other whole protein)
• Intractable malabsorption
• Feeding difficulties in post-op conditions
• Chronic intestinal disease (e.g. Crohn’s disease)
• Short bowel syndrome following intestinal resection

Children and adults

An unflavored, powdered mixture of essential and non-essential amino acids.

Not nutritionally complete.

Phlexy-Vits
(a powdered vitamin and mineral preparation)

• Restrictive therapeutic diets

Individuals over 11 years of age

A concentrated, powdered vitamin, mineral and trace element preparation to meet the micronutrient requirements

Flavor Packets
(cherry-vanilla, grapefruit and lemon-lime flavors.  

• May be used with any of our powdered products for greater variety and diet compliance

Children and adults

Powdered 5 g flavor packets