An isoleucine-, leucine- and valine-free powdered medical food for the dietary management of maple syrup urine disease (MSUD) in older children and adults, including pregnant women and women of child-bearing age.
This formulation is available in the US and Canada.
Main Features:
Isoleucine-,
leucine- and valine-free
Contains
a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, vitamins, minerals and trace elements.
MSUD
Maxamum provides 40 g of protein equivalent per 100 g of
powder
Pleasant
orange flavored powder
Does
not contain fat thereby allowing greater flexibility in modifying
energy intake.
Indications:
Maple Syrup Urine Disease
Directions for Preparation and Use:
Maxamum must be consumed in conjunction with natural protein, fluid and
other nutrients in quantities prescribed by a physician or dietitian
to meet protein and general nutrient requirements.
The
recommended intake of Maxamum will vary depending
on the age, bodyweight and medical condition of the individual.
Intake should be adjusted to maintain normal growth and development.
For accuracy, Maxamum should be weighed on a gram
scale. The daily intake of Maxamum should be divided
into equal portions and distributed throughout the day.
Maxamum is best served with meals. Make a paste of the prescribed
amount of powder with a small volume of chilled water. Gradually
add sufficient water to make the desired volume. It is recommended
that Maxamum be prepared at a 1 to 7 dilution
(e.g. 35 g (approx ¼ cup) of powder plus 245 mL (approx.
8 fl oz) of water) and advanced to a 1 to 5 dilution (e.g.
35 g (approx ¼ cup) of powder plus 175 mL (approx.
6 fl oz) of water). These dilutions are guidelines only. Maxamum may be given in a more concentrated
form (e.g. drink or paste). If so, water or diluted drinks
should be offered at the same time. For best taste, consume
immediately. Larger volumes of prepared drink mix should
be refrigerated and used within 24 hours or preparation.
Maxamum
Range
Measure
Weight
1
Cup
145
g
1/2
Cup
70
g
1/4
Cup
35
g
1
Tbsp
9
g
Precaution:
Must
only be consumed by individuals with proven maple syrup
urine disease while under strict medical supervision.
Not intended for children under nine years of age. Not
suitable as a sole source of nutrition. Not for parenteral
use.
Storage:
Store
unopened can at room temperature. Do not store at extreme
temperatures. Once opened, reseal can and store in a cool,
dry place (not in refrigerator) and use within one month.
Metabolics
